Cystic Fibrosis - Iimpawu

Njengomthetho, kunokwenzeka ukuxilonga i-cystic fibrosis esemncinci, kuba ibonakaliswe ngumqondiso ophawulekayo. Kodwa ngohlobo oluthile okanye oluphuculweyo luhlobo oluthile, lesi sifo sibonakaliswa kakuhle. Ngoko ke kubalulekile ukwazi, ukuze kuhlukaniswe kwezinye izifo ezifanayo ngqo kwi-fibrosis ye-cystic - iimpawu kunye neempawu zayo zangaphandle.

Izifo ze-cystic fibrosis - yintoni na?

Isifo esikulo mbuzo, kunoko, sisifo. Kuvela ekutshintshisweni kwemfuza ekhoyo kwingalo ende ye-chromosome yesixhenxe. Ubunokwenzeka bokugula kuphela ukuba ngabazali bobabini bayithwala imfuyo eyonakalisiweyo, kwaye i-25%. Nangona le miqathango, isifo se-cystic fibrosis sichaphazela inani elaneleyo labantu, kuba i-chromosome eneentshukumo zikhoyo kubo bonke abahlali abangama-20 emhlabeni.

I-Cystic Fibrosis kuBantu abadala - Izibonakaliso

Njengoko sele kuphawuliwe, isifo sibonakaliswe ebuntwaneni, ngokuqhelekileyo ukuya kwiminyaka emi-2, kwaye kuphela i-10% yezigulane ezinezibonakaliso zokuqala zibonakala zikhulile kwaye zikhulile.

Impawu eziphambili ze-cystic fibrosis zi:

Izimpawu ezibhalwe kwi-cystic fibrosis zihambelana nokuba i-gene elimelekile ayivumeli ukuba umzimba uvelise iprotheni ejongene nekhosi eqhelekileyo yamanzi-electrolyte metabolism kwiiseli zamalungu angaphakathi. Oku kukhokelela ekunyuseni koxinano kunye ne-viscosity ye-fluid eveliswe ziintlanca ze-secretion yangaphakathi. I-Mucus igxuma, iibhaktheriya zanda kulo, kwaye utshintsho olungaphendukiyo luvela kwizitho, ngokukodwa kwimiphunga.

Ifomu le-intestinal ye-cystic fibrosis ibonakaliswa ngokuqhaqha, ukugubha, ukugcoba nokuhlanza. Lezi zimpawu zithinteka unyango ngokuthatha amachiza kunye ne-enzymes, kodwa ukubonakaliswa kwempompo yesifo kuyaqhubeka ukwandisa.

I-Cystic Fibrosis - I-Diagnosis

Okokuqala, ubukho beempawu eziphawulekayo zesifo zihlolwe - i-viscosity yemfihlelo yamalungu angenanto yangaphakathi, ukunyuka kwezifo ezingapheliyo zenkqubo yokuphefumula. Emva koko, kuyimfuneko ukuseka ubukho bemfuyo eguqulwayo kubazali kunye nokujonga iimeko zokuxhatshazwa kwintsapho.

Uhlalutyo oluchanekileyo lwe-cystic fibrosis yi-DNA. Olu vavanyo lulona lukhuni kakhulu, kwaye luyakwenziwa nangona ngexesha lokukhulelwa ngokuhlola i-amniotic fluid. Inani leempembelelo ezingamanga lidlulile kwi-3% kwaye likuvumela ukuba uhlolisise ngokukhawuleza ngaphandle kwemilinganiselo eyongezelelweyo.

Ukuchonga inani lamathambo e-fatty kunye ne-chymotrypsin kwisigulane sesigulane kuyindlela enye yokufumanisa esi sifo. Izikhombisi eziqhelekileyo ze-chymotrypsin ziphuhliswa ngabanye kwibhubhoratri nganye. Isixa sama-acids esenza ukuba ukusola kwe-cystic fibrosis ingaphezu kwe-20-25 mmol ngosuku.

Uvavanyo lwe-swestic fibrosis kunye ne-pilocarpine luhlolisiso lwe-chloride e-liquid efihliweyo. Uvavanyo kufuneka luvavanywe ubuncinane kathathu ukuze kusetyenziswe ukuxilongwa ngokuchanekileyo.