Bullous pemphigoid

I-Bullous pemphigoid okanye isifo sikaLever sisimo esingapheliyo sezilonda zesikhumba kunye nokubunjwa kwe-blisters. Ngokuqhelekileyo, esi sifo senzeke kubantu abadala, abaneminyaka engama-60 nangaphezulu. Kule meko, i-pemphigoid inobunzima, kwaye umfanekiso weklinikhi ufana ne-pemphigus ene-vulgar, enokuthi ibe yinkimbinkimbi ye-diagnostic and process process.

Iimpawu zenkomo ye-bullphi pemidgo

Ngokuqhelekileyo isifo sichaphazela isikhumba se-trunk kunye nemigqomo, ngokugqithiseleyo i-pemphigoid ihlanganisa izicubu zentloko, ubuso kunye nezinkulu zemvelo. Isiqhamo sesifo sikaLera siyiziphulo ezilinganayo, oku:

Ziqukethe umbane ocacileyo, ovalwe ngamathayi athathaka. Akuqhelekanga kwesikhumba apho i-blisters ibonakala ibe nombala ophilileyo, kodwa ngokuphindaphindiweyo ihamba ihamba ne-redness, eyona nto ibonisa isifo. Umfanekiso weklinikhi uncediswa ngamabhanti ahlukeneyo, angabonakalisa ngephutha i-sarcoidosis.

Iimpawu ezibhalwe apha ziphambili kwaye ziyazibonakalisa ezinsukwini ezimbalwa zokuqala, emva koko i-rash kunye ne-blisters zivuliwe kwaye iziphene ezinobulantshi ezinobunzima zenziwa kwindawo yazo. Kwimeko ye-pemphigod ye-bulls, izilonda azange zihlanganiswe ne-crusts, kodwa zi-epithelialized.

Kwakhona kubalulekile ukuba kwisinye sezigulane ezi-5 ukugqithisa kubandakanya kakhulu umlomo we-mucosa kwaye emva koko kubonakala kwesikhumba.

Unyango lwe-bullous pemphigoid

Ubungqina bonyango lwe-bullfu pemphigoid okanye i-Lever's disease usele kwinto yokuba kufuneka kube nzima kunye nomntu ngamnye. Oogqirha bakhetha i-regimen yonyango ngokusekelwe kwimiba elandelayo:

Kodwa nangona kunjalo, iindlela eziphambili zokuphatha isifo sikaLever ziyizidakamizwa eziqukethe i-glucocorticosteroids. Ekuqaleni kwonyango, izigulane zinika umlinganiselo we-60-80 mg weyeza kwiiyure ezingama-24. Emva koko, ugqirha, ngokuqwalasela idatha engentla, utshintshe umthamo.

Kwakhona kusetyenziswa unyango lwe-pemphigoid, i- immunosuppressants kunye ne-cytostatics. Ezi zi yobisi zivimbela ngokukhuselekileyo ukhuseleko, kwaye zisuse isisu. Ngokuxhomekeka kobunzima beempawu kunye nesigaba sokuphuhliswa kwabo, i-enzyme ye-systemic iyalelwe, amalungiselelo enziwe kumxube we-enzyme zityalo kunye nezilwanyana ezichaphazela iinkqubo zokuvuvukala, iinkqubo zokubuyisela kunye nezimpendulo ze-immune. Ngaloo ndlela, imeko yesigulane iphuculwe kakhulu.