I-Myopathy isifo esingahleliyo se-neuromuscular esibangela ukulimala kwemisipha yomzimba. Isizathu sentsholongwane sisifo sengxaki . Uphando olusandululwazi lwakutshanje lubonisa ukuba iimbumba ezinokukhubazeka zenziwa kwiiseli ze-muscle, kwaye ii-fibers zilahlekelwa yi-amino acid ezifunekayo, i-enzymes, i-creatine, ziyabhujiswa zife.
Izibonakaliso zengqondo
I-Myopathies ifaka phakathi kwezifo ze-neuromuscular heritage and syndromes neuromuscular kwizifo ezithile ze-somatic ne-neurological. Impawu eziqhelekileyo zazo zonke iintlobo ze-myopathy zibuthathaka kunye nezifo.
Iimpawu zeDuchenne myopathy
Isifo esixhaphakileyo sisifo siyi-myodystrophy yaseDuchesne. Kukho isifo kuphela kumakhwenkwe kwaye sisasazwa nge-gene pathological obtained from mother. Sekuqaleni kwiminyaka yokuqala yobomi kukho ukulahlwa kwezakhono zamandla, ubuthathaka bemisipha yendawo ye-hip. Kwixesha elizayo kukho ukunyanzeliswa kwezihlunu ze-trunk kunye nebhinqa lamagxa, kunye nemisipha yokuphefumula. Kukho i-lordosis (i-pathology ye-spine), ukuxhaswa kwemisipha yamathole. Ekuqaleni kwasebuntwaneni, uninzi lwezigulane ziyeke ukuhamba ngokuzimeleyo, zihlakulela iimpawu zesifo sengqondo, ingqiqo ayihambelani nemimiselo yeminyaka, isisu somzimba sisiphazamiseka. Izigulane aziphili ixesha elide, zifa ngexesha elineminyaka engama-30 ngenxa yesifo senhliziyo okanye ukungasebenzi kwempompo.
Iimpawu ze-steroid myopathy
Isizathu se-syoidathy myopathy yinyanzelo eyongezelelweyo ye-glucocorticosteroids egazini ngenxa yokuveliswa ngokweqile kwe-correx yabo ye-adrenal. IHormones inokunyuka nakwizigulane ezifumana i-glucocorticosteroids ixesha elide kunyango lwezifo ezahlukahlukeneyo. Iingxaki eziphambili zekliniki zidibaniswa nenguqu ekubonakaleni kwesigulane. Kuyacaca ukuba ukuthunyelwa kweesitifiketi ebusweni, entanyeni, emzimbeni ophezulu (ngokukodwa kwi-clavicles). Inxalenye engezantsi yomzimba ayitshintshi, ekhokelela ekungabikho komzimba ngokucacileyo. Izigulane ziva ubuthakathaka obunamahlunu kunye neentloko, zipholisa amanxeba ngokukhawuleza, zikhona izifo ezithathelwanayo. Isici esichaphazelekayo yi-striae-welula amanqaku elukhumbeni, ephuma kwi-fragility yenyuka yamathambo. Abantwana banenkathazo yokukhulelwa kokukhula, kubantu abadala kukho ukuphazamiseka kwesondo. Izigulane ze-steroid zengqondo zithinteka ukuxinezeleka, iingxaki zokuqonda.
Iimpawu zokunxiliswa kotywala
Ulwaphulo olunxilisayo lubonakala kubantu abasebenzisa kakubi utywala. Ngenxa yempembelelo enobungozi ye-ethyl emzimbeni, iiseli zeemfibisi ze-muscle zamathambo kunye nezitho zangaphakathi ziyafa, kwaye i-necrosis encinci iyaqhubeka. Izidakwa zihlala zikhalaza malunga:
- ukukhathala;
- ukunyanzelwa kweminwe neenzwane;
- ukuvakalelwa kobunzima kummandla wesibeleko.
Kwaye kukho ubusuku benkampu , ukuphulwa koqhagamshelwano. Iba yinto ephawulekayo yezandla. Imisipha yancinci ibe yinto ephazamisayo, i-lethargic, ayikwazi ukuxhatshazwa. Indlela yokwenza utywala obunxilisayo kubonakalisa ufana neempawu zenye i-myopathies.
Kubalulekile ukuba xa kubonakala iimpawu zogqirha-myopathy, zixilonge ngokukhawuleza