Isifo sikaBehcet sisifo esihlala sisigxina, isifo esiqhelekileyo eJapan naseMeditera. Ininzi idla ngokuqhubekayo kubantu abaneminyaka engama-30 ukuya kuma-40. Esi sifo singeqela le-vasculitis kwaye li-etiology engacatshangwanga.
Izizathu zeZifo zeBehcet
Ukuphuhliswa kwesi sifo kudibaniswa neziganeko ezininzi zokuqala, phakathi kwezi zinto zilandelayo:
- imfuza;
- i-herpes kunye ne-infection ye-streptococcal ;
- ngxaki.
Uninzi lweengcali zikholelwa ukuba ukuqaliswa kwesifo seBehçet kubangelwa zizifo ezithintekayo, kwaye kwixesha elizayo, iinkqubo ezizimeleyo zixhomekeke kubo, kunikezelwe ukuzalwa.
Iimpawu zesifo seBehcet kubasetyhini
Esi sifo sibonakala nge-polysimptomicity. Kule meko, iimpawu eziphambili, apho unokwenza uvavanyo oluchanekileyo, zidibene nomonakalo kwiimbumba zomlomo kunye nezitho zangasese, kunye neenkqubo zokuvuvukala emehlweni. Cinga zonke iimpawu zesifo seBehçet ngokubanzi.
Umonakalo womlomo womlomo
Ekuqaleni, iincinci ezincinci ezinezinto ezinamafu zivela emlonyeni, esibhakabhakeni, ngolwimi, kwizinsini, kwi-pharynx, ngaphakathi kwimihlathi, ezivulwayo. Esikhundleni se-vesicles, ijikelezo, izilonda ezibuhlungu (aphthae) zombala obomvu obomvu zenziwe, ubukhulu bayo bufike kwi-2 cm ububanzi. Ukuphilisa izilonda kwenzeka emva kwenyanga, kunye nezihlandlo ezi-3-4 ngonyaka ngokuphindaphindiweyo kwezilonda.
Izilonda zomzimba
Abasetyhini kwi-membrane ye-vagin ye-vagina kunye ne-vulva ifom, izilwanyana zibuhlungu, zifana nezo zivela emlonyeni. Emva kokuphilisa, iinkohlakalo zihlala zihlala kwindawo yazo.
Ukuphazamiseka kombono
Ezi zibonakaliso zivela emva kweeveki emva kweempawu emlonyeni womlomo. Izigulana zikwazi ukuhlambalaza iris iris and bodyiliary body of eyeball, ukuvuvukala kweembandezelo kunye neembilini zehlo, ukuvuvukala kwe-cornea. Ngokuqhelekileyo kukho iimpawu ezilandelayo: i-photophobia, umbono obonakalayo, ukunyuka ukukhala.
Ukubonakaliswa okukodwa
I-erythma ye-nonodular, i-pyoderma, i-papulo-i-rashular eye iyakubonakala. Kwakhona kwezinye iimeko, iindleko zokulahleka kweenwele, i-panaritium yesikhombiso iyaqwalaselwa.
Iintlupheko zesistim se-musculoskeletal
Kukho ukuphuhliswa kwesifo samathambo (amaninzi amanqanaba angaphantsi) ngaphandle kwezinto eziwonakalisayo.
Izimpawu ze-neurological
Kukho iziganeko zomonakalo weentsimbi zomhlaba, ukuphuhliswa kwe-meningoencephalitis, i-edema ye-optic nererve disk, ukubonakala kwe-hemiparesis.
Utshintsho oluthile lokutshiza
Impawu yokuphuhliswa kwe-vasculitis, thrombophlebitis yeemvini emilenzeni, i-thrombosis ye-veptic veins kunye ne-thromboembolism ye-pulmonary umthambo, i-aortic aneurysm, njl njl.
Ngeentlungu zesisu esiswini, intliziyo nemiphunga, kunokukho iimpawu ezinjalo:
- isicefe
- isifo sohudo;
- hemoptysis;
- intlungu entliziyweni, njl
Unyango lweZifo zeBehcet
Ukunyangwa kwesifo seBehcet, okokuqala, kuhloswe ukukhulisa ubomi bogulane, ukuphumeza ukuxolelwa kwexesha elide nokukhusela ukutshintsha okungenakuguquka kwizitho zangaphakathi.
Ukubonakaliswa kwezilonda ezinobungozi be-Behcet's syndrome kwisigodlo somlomo kunye nasezintweni zobuncwane ziphantsi kwonyango lwendawo kunye nokusetyenziswa kwe- glucocorticosteroids , izisombululo ze-antiseptic, kunye namaxesha athile-ama-antipodal agents. Kwakhona ukunyangwa kwesifo, i-cytostatic agents, immunosuppressors, iivithamini zinokumiselwa. Umonakalo we-Vascular uphathwa ngeendlela zokugqirha. Izigulane ezininzi zichazwe i-extracorporal hemocorrection. Unyango luyenziwa phantsi kolawulo lwezonyango rhoqo.