Abantwana-i-Butterflies ... Ngexesha lokuqala ukuva eli binzana, baninzi banokukhawuleza bacinga amabhu ambala, bengenaxhala phakathi kweentyantyambo kunye novuyo lwabantwana, abangenalo ukudumala nokuxhalabisa. Okwangoku, ubomi bezingane ezine-butterfly syndrome akufani nento yamagama okanye umfanekiso ococekileyo. Kule nqaku siza kuthetha nge-congenital bullous epidermolysis - isifo esingaqhathaniswa nesifo sofuzo esibangela ulusu lomzimba womntu.
I-Epidermolysis yeBullous: Izizathu
Njengomthetho, abazali bebhathane besafunda malunga nokugula kwesikhumba somntwana kwiintsuku zokuqala (kunye neeyure) emva kokuzalwa komntwana. Ngesihlandlo sokuqala esi sifo sichazwa nje ekupheleni kwekhulu le-19, ngo-1886.
Isizathu sesifo sisisiphako semfuyo esinqanda isigaba se-epidermal sokukwazi ukwenza umsebenzi okhuselekileyo. Esi siphene sihanjiswa kubazali abafihliweyo, okanye kuvela ngokukhawuleza. Ngenxa yoko, yonke isikhumba (kubandakanywa iimbumba ezinqamlekileyo) ziba nzima kakhulu - ukuthintana okuncinci kungabangela umonakalo. Ngaphandle koko, abantwana abanjalo baqhelekileyo - abagqali emva kokuphuhliswa ngokomzwelo nangokwengqondo, bakhula ngokuqhelekileyo kunye noncedo abanokuba yinxalenye epheleleyo yoluntu.
Iipatheni zelifa lesi sifo azikabonakalwanga - izigulane ezine-bullid epidermolysis zinokubantwana abanezempilo kunye nabagulayo. ukungaqhelekanga kwesi sifo kukuthi ngaphambi kokuzalwa komntwana akunakwenzeka ukuyixilonga yiyiphi na indlela yezokwelapha eyaziwayo - akukho i- ultrasound ye-fetus okanye iimvavanyo zelabhoratri ezivelisa iziphumo.
Ixesha elibalulekileyo lobomi kubantwana bebhabhathane liyiminyaka emithathu. Kwixesha elizayo, ngokunonyango olufanelekileyo kunye nokunyamekela, ulusu luba yinto encinci, luba luzinzile, nangona alufinyeleli ngamandla kwesikhumba somntu ophakathi. Ukongezelela, abantwana abancinci abakwazi ukuqonda ubudlelwane obangela umphumo, abakwazi ukuchaza ukuba akunakwenzeka, umzekelo, ukukhwela ngamadolo abo, kuba isikhumba semilenze emva koko "siphume" ngokupheleleyo, okanye ugubungele amehlo okanye izihlathi.
I-epidermolysis ye-Bull: unyango
Ingxaki yabantwana be-butterfly inzima, kuba ukugula okubangela ukuba bahlupheke kangako namhlanje. Yonke into enokuthi yenzelwe iintsana ezinjalo kukuzama ukukhusela isikhumba sabo esikhathekekileyo ekukhuseleni (okunzima kakhulu), kwaye xa kwenzeka ukuba kulungile kwaye kufike ngexesha lokuzijonga. Kodwa nangona kunjalo, kumazwe amaninzi aphucukileyo amaziko okunyamekela izigulane kunye nezifundo zonyango oluqhubekayo, eziye zabenza ukuba zikhokele ubomi obuqhelekileyo, ukufumana imfundo, ukuqhuba ubomi bentlalo kunye nokudlala imidlalo.
Kwi-CIS, kunye nokuxilongwa kwe-bullid epidermolysis, ukugqalwa kwesigxina kudla ngokungahambi kakuhle, ngenxa yokuba isifo siqabile kakhulu, oogqirha abanakho amava ukuba baphathe izigulane, kwaye kwezinye iimeko abaze bakrokre ukuba kukho esi sifo. Ngokuqhelekileyo abazali ngokwabo baxhatshazela imeko, benza iyeza kunye nokuzama ukuphazamisa umonakalo kwintsholongwane yentsana ye-phytotherapeutic, amafutha okugcoba kunye nabathethi, i-bluehead nezinye iindlela zolu hlobo. Akufuneki ukuba, emva kokuba "unyango" olunjalo, iindleko zokubuyisela i-epidermis yokunyuka komntwana kwimizimba ye-cosmic, ngelixa ukhathalelo olufanelekileyo ngexesha elifanelekileyo kunzima nakakhulu, kodwa lubiza kakhulu. Iintsholongwane zidinga
Ngenxa yokungabikho kolwazi olwenziwe ngonyango kunye noluntu, ukungabi nolwazi kolondolozo kunye nenkango, abaninzi abantwana abane-bullid epidermolysis bafa beselula.
Enyanisweni, ukunakekelwa kwesikhumba kunye nendlela yokuphila yabantwana bebhathane behluke kakhulu ngokuxhomekeke kwisibandezelo sesi sifo - esona sibi kakhulu kwaye sichaza ngakumbi iimpawu, ukunyamekela kunye nokuchaneka kunyango kunye nokunyangwa komntwana kufuneka kube.