Phakathi kwezifo eziqhelekileyo ezibangelwa ukuguquka komzimba, i-cystic fibrosis yamaphaphu iphezulu kwoluhlu. Le nzala ihambelana nokuphulwa komthetho ofihliweyo ngamalungu angaphakathi, okukhokelela ekutshitshweni kwenkqubo yokuphefumula kunye nesondlo sesisu.
Isifo se-Genetic se-cystic fibrosis
Isifo esibuzwayo sibizwa ngokuba yi-cystic fibrosis. Ubonakaliswa ngophakamileyo oluphezulu kunye ne-viscosity eqinile ye-mucus, ehlanganisa izitho ezingenanto. Njengomphumo wale nqubo, ukuvalwa kwemfihlo, kunye neebhaktheriya ze-pathogenic ezibangela ukuvuvukala ngokuphindaphindiweyo.
I-cystic fibrosis yompompo inobangela omnye-umonakalo kwi-chromosome yesixhenxe (ingalo ende). Ngokwezibalo, umphathiswa wesi sifo ngumntu onamashumi amabini kwiplanethi. Ubungakanani besi sifo ngu-25%, ngaphandle kokuba abazali bobabini banomzimba owonakele.
Kukho iintlobo ezi-3 zezi zifo:
- intestinal cystic fibrosis;
- i-pulmonary okanye i-cystic fibrosis;
- uhlobo oluxutywe (i-pulsary cystic fibrosis).
I-Cystic fibrosis yemiphunga - iimpawu
Impawu eziphambili zesifo:
- ukugqithiswa kweentlanzi, ezixubileyo ngexesha lokukhwehlela;
- ukuqhuma kwexesha lokuqhuma kwe-pneumonia, i-bronchitis, i-pneumonia;
- ukuphazanyiswa kwamathumbu;
- ukupheliswa kwamanzi;
- intlungu, ukungathandeki kwisisu;
- ukwandisa ukondla ngobunzima obaneleyo kunye nophuhliso lomzimba;
- izifo zesini;
- pancreatitis ;
- ukuqina kweminwe ezandleni;
- isifo sesibindi;
- isifo sikashukela;
- sinusitis ;
- ukuhlukana kwamathambo;
- ukubola kwesisu (ngqo).
Ifomu ye-pulsary ye-cystic fibrosis ibonakalisa kwiminyaka emibili yobomi, ibonakaliswa ngumlinganiselo omkhulu wokufihla phakathi kunye ne-bronchi encinane yomntwana.
I-Cystic Fibrosis - Ukuxilonga nokuhlalutya
Ukuxilongwa kwenziwa ngeendlela ezine eziphambili.
Okokuqala, ubukho bomzimba obonakele kubazali kunye neemeko zeziganeko zentsapho zihlolwe. Iziphumo ezintle, kunye nokufumanisa iinkqubo ezingapheliyo zokuvuvukala emiphakeni kunye ne-bronchi, ubukho be-intestinal syndrome, bangela ukuba kuqhutywe uvavanyo lwe-sweat. Iqulethe ekuqingeni izinga leetyule kumanzi okhutshwe yii-pores. Ukwenza inkqubo, inxalenye encinci engalo (ingaphezulu kwendlovu) iphathwa ngeziyobisi ezikhethekileyo ezibizwa ngokuba yi-pilocarpine. I-electrode iqhotyoshelweyo kule ndawo, ikhupha ukukhululwa kwesithukuthezi, esicaciswe yiplastiki okanye i-tishu egcina ukufudumala, ukudala umphumo we-sauna. Emva kwemizuzu engama-40, ukuveliswa kwamanzi kuhlalutya koluhlaza. Ukuba izinga lalo lidlula imida ebekiwe, ukuxilongwa kokugqibela kwenziwa.
I-cystic fibrosis yamachiza emiphunga
Ubume besifo asivumeli ukuba unyange ngokupheleleyo, unyango lujoliswe ekuphelisweni kwempawu kwaye lufuna indlela edibeneyo. Unyango luquka imisebenzi elandelayo:
- iikholeji ezinde;
- kwi-mucolytics;
- kinesitherapy;
- Inhalation ye-corticosteroid hormone kunye ne-beta mimetics;
- ukusebenzisa i-bronchodilator;
- ukwenza ukuphefumula;
- Ukulungiswa kokutya kunye nokwanda kwesikhokelo samalanga ngama-10-15%;
- umjelo wamanzi wamaphaphu;
- i-bug-massage;
- ukwamkela iivithamini kunye ne-microelements.
Eyona mivuzo kwaye iphumelele ngethuba lonyango indlela yokwelaphulwa kwemiphunga. Ukongezelela, uphando lwenzululwazi luqhutyelwa rhoqo ukulungisa i-gene ewonakalisiweyo ngokuguqula iipilisi ezenziwe ngokufanelekileyo.