I-Amyloidosis ibonakaliswa ngokuqokelela kwiprotheni engaqhelekanga emzimbeni. Ngexesha elifanayo kwiimeko eziqhelekileyo akukho emzimbeni. U-Amyloidosis unempawu, apho kunokwenzeka ukucacisa ubungakanani kunye nokuxakeka kwesi sifo.
U-Amyloidosis wezitho zangaphakathi
Xa isifo sifana, iprotheni engaqhelekanga iqokelela, eyabangela ukwakheka kwamanantibobodies. Emva kokusebenzisana kwe-antigen kunye ne-antibody, iprotheni eyenza i-amyloid precipitates. Kwixesha elizayo, unokususa izinto ze-organ, ezikhokelela ekufeni kwakhe ngokupheleleyo. Isifo sinokuchaphazela zonke izitho zangaphakathi ezibalulekileyo, umzekelo, intliziyo okanye amathumbu.
Iimpawu ze-amyloidosis zamathumbu:
- ukungaxakeki kunye nobunzima besisu;
- buhlungu kunye neentlungu ze-spasmodic;
- ukutyunjwa okanye urhudo;
- igazi legazi
- leukocytosis;
- hyperglobulinemia;
- hypoprothrombinemia;
- i-hypocalcemia.
I-Amyloidosis yentliziyo iphazamisa ukunyaniseka kwezicubu, kwaye idibanisa ukuphazamiseka kwentliziyo kunye nesantya senhliziyo. Iqumrhu lingakwazi ukupompa inani elifunekayo legazi kwaye ngokuqhelekileyo ligcina igazi linikezelwa kumzimba womntu. Iimpawu eziphambili zesi sifo zi:
- ukuphefumula okufutshane ;
- ukuvuvukala;
- buthathaka;
- isicefe
- i-arrhythmia.
I-Amyloid inokuchaphazela neentsholongwane. Ukubonakaliswa kwe-amyloidosis yentsholongwane yendawo yilezi zilandelayo:
- ukubetha nobuthathaka kwimisipha;
- ukuphazamiseka kwemali;
- utywina xa u eme;
- ukuphulwa kolawulo lokucoca kunye nokuchaswa;
- ukubetha kwizandla.
I-Amyloidosis yolusu
Zininzi iintlobo zezilonda zesikhumba:
- i-amyloidosis yangundoqo yesikhumba;
- i-amyloidosis yasecaleni yesikhumba;
- I-amyloidosis yendawo yesikhumba kunye ne-amyloidosis epheleleyo.
Ngesi sifo, ezininzi, ezinobunzima, ezinamahlunu ezincinci zibonakala kwesikhumba, esoloko sitshisa. Zincinci ngobukhulu kwaye ziluhlaza kwaye ziluhlaza ngombala.
I-disk i-amyloidosis i-discs ibonakala ixakeke kumgca kwaye inobumba obumnyama obumnyama. Ngokudla kaninzi, kubonakala kubantu abagula ngesifo sofuba, i-malaria, izilonda zesikhumba kunye nama-abscesses.
I-amyloidosis yendawo ingabonakalisa njengamaphepha amancinane, umzekelo, emlenzeni ongezantsi, kaninzi ngaphantsi kwezinye iindawo zomzimba. Zibonakala ngathi zinamaqabunga amancinci okanye iipilisi ezixubileyo ezikufutshane eduze komnye nomnye. Kukho ukubetha okuphawulekayo.