Lyell's Syndrome

I-Lyell's syndrome (igama lesibili nguStevens-Johnson syndrome) yindlela ephikisayo yokuguqula umzimba, ibonakaliswe kwintambo kunye nokufa kwesikhumba esingaphezulu, kunye nokuxiliswa komzimba wonke ngenxa yokuphendula okuqhubekayo. I-Lyell's syndrome ithathwa njengesihlandlo sesibini esiyinkimbinkimbi emva kokutshatyalaliswa kwe-anaphylactic ngenxa yeso simo esivela ekuxhaseni komntu kwizinto ezithile. I-Lyell's syndrome, ebizwa ngokuthi "i-epidermal necrolysis", yaqala ukuchazwa ngowe-1956, kodwa ngoku kubekho ukungavumelani kwiindawo zonyango malunga nokuqala kwesi sifo.


Iingxaki zeLyell's Syndrome

Kwiimeko ezininzi, i-Lyell's syndrome ivela njengesifo sengqondo:

Kwezinye iimeko akunakwenzeka ukuseka izizathu ezithile zokusabela kwe-idiopathic, kodwa, njengengqapheli yengcali, iqela elijongene nobungozi lubandakanya abantu abahluphekayo:

Iimpawu zeLyell's Syndrome

Isifo ngokuqhelekileyo siqala ngokukrakra kwenyusa izinga lokushisa kwama-40 degrees okanye ngaphezulu. Kule meko, isigulane sibhekene neentloko ezinzima nentlungu. Ukuphazamiseka kunye nehudo kuphawulwe. Emva kwexeshana, ukugqithisa kubonakala kwesikhumba, kufana nokuqhaqha kwimasisi kunye nomfutho obomvu, uhamba kunye nokuvuna okanye ukuva. Okokuqala, iindawo ezinomlilo ezinokutsha zihlala kwindawo yangasese kwaye kwindawo yendawo yokuxhoma, kwaye ngokukhawuleza baqala ukuhlala kuyo yonke indawo yomzimba.

Isici esichaphazelekayo se-Lyell's syndrome yinkampani ye-skin epidermis kunye noqhagamshelwano oluncinane nolusu lwesigulane. Oku kuvula ukukhutshwa kwamanzi okwehla. Kwiindawo ze-erythm, i-bubbles yenziwe, evulekileyo, evulekileyo, ibonakalise iindawo ezinkulu ezikhulayo kunye ne-serous exudate. Usuleleko lwesibini oluhambayo lubangela ukukhukuliswa kokukhupha, okubangela ukuvumba okwenzisayo kumzimba. Iimbumba ezinomlomo emlonyeni, amehlo kunye nezitho zangasese nazo zineenguqu ezimbi. Ingozi enkulu kwimpilo nobomi imelwe ngu:

Unyango lwe-Lyell's Syndrome

Xa kukho izibonakaliso zesifo, kufuneka usheshe ubiza i-ambulensi. Isigulane sifakwa kwiyunithi yonyango enzulu okanye kwiyunithi yokunyamekela. Iimeko zokuhlala ngexesha elifanayo zifana nezo zidalwa kwizigulane ezitshisa kunye neqabunga. Imfuno ebalulekileyo yokunyamekela kunye nokunyanga yinyumba. Umbutho wonyango kwi-Lyell syndrome ngolu hlobo lulandelayo:

  1. Ukupheliswa kwazo zonke iziyobisi ezisetyenziswa ngaphambi kokuphuhliswa kwesifo.
  2. I-Glucocorticosteroids imiselwe.
  3. Uhlobo olushushu luphathwa ngeoli yemifuno kunye ne-vitamin A.
  4. Izicombululo ze-Saline kunye ne-colloidal zicetyiswa ukuba zizalise umbane olahlekelwe ngumzimba.
  5. Ukusetyenziswa kwamanzi
  6. Xa ujoyina isifo sesibini, i-antiseptics kunye ne-antibiotics zisetyenziswa.

Ixesha elifanelekileyo kwaye liqhuba ngokuchanekileyo unyango lunceda ngokukhawuleza ukufumana isigulane nesifo sikaLyell.