I-vasculitis engama-hormone kubantwana

I-vasculitis engumzimba isifo esichaphazela kakhulu i-capillaries yeekhumba, kunye nemithambo yegazi yesigxina sokugaya, izilwanyana kunye nezintso. Yingxowankulu ye-immunocomplex i-vasopathies ye-allergentic ye-infectious nature. Ukuqala kokuphuhliswa kwesi sifo kunokwenzeka nanini na ubudala, kodwa, ngokomthetho, abantwana abancinci (uneminyaka engama-3 ubudala) bahlupheke kakhulu kwesi sifo kakhulu.

Ngokuqhelekileyo, i-vasculitis ifumaneka kubantwana abaneminyaka engama-4 ukuya kwe-12.

Kukho iintlobo ezininzi ze-vasculitis eziqhekezayo, ezahlukileyo kwimbonakalo yazo kunye nemvelo. Ngaloo ndlela, i-vasopathy ihlukaniswe ngamagqabini amabini: i-Hippel-Landau isifo, i-Ehlers-Danlo syndrome, i-Kazabaha-Merrita syndrome, iLouis-Bar, njl.) Kwaye ifunyenwe (i-vasculitis ephawulekayo kunye nokudityaniswa kwemvelo eyahlukeneyo, isetyhi, i-hypovitaminous and infectious vasopathies, njl).

I-Vasculitis isisu: izizathu

Esi sifo sibangelwa umonakalo kwiindonga ze-capillary kunye nokwanda kwintlepheko yeempahla ngokubanzi, kunye nokusebenza kwenkqubo ehambelanayo kunye nokwanda kwenani le-immune complexes ekhiqizwayo.

Ngokuqhelekileyo, ukuphuhliswa kwesi sifo kuqala ixesha elide emva kwesifo esithathelwanayo (i-ARVI, i-tonsillitis, i-red fever, njl.). Ngamanye amaxesha ukuphuhliswa kwe-vasculitis kulandelwa ukunyanzeliswa kwezidakamizwa (okanye ezinye iintlobo zokuphendula ngokuthe tye), i-hypothermia, ugonyo, ukugonywa.

Iimpawu ze-vasculitis kubantwana

Kwiimeko ezininzi ezininzi, isibonakaliso sokuqala sesi sifo sibonakala ngathi ukukhwabanisa kwesikhumba sombala obomvu. I-Foci ye-rashes: iifolda zeengcambu, izibonda, indawo ejikeleze amajoyina. Ngokuqhelekileyo zibonakala zihlahlela ebusweni, iintendelezo kunye neenyawo, isiqu. Emva kokugqithisa kwexesha, amabala amnyama ahlambulukileyo ahlala kwindawo yawo, eqala ukupheliswa ngokuphindaphindiweyo kwesi sifo.

Uphawu olulandelayo oluqhelekileyo luyimonakalo edibeneyo. Kuyabonwa kwiveki yokuqala yokugula. Ubume kunye nobude bentlungu buyahluka kakhulu, amaninzi amakhulu amaninzi, ngakumbi i-ankle kunye namadolo, achaphazelekayo. Kule meko, ukuxhamla okudibeneyo, kodwa akukho ukuguqulwa komsebenzi kunye nokuphazamiseka kwezicubu ezingenakunyaniswa.

Uphawu lwesithathu oluqhelekileyo luyintlungu yesisu. Ungabonakalisa okanye unqobe ilusu namalungu. Ukuhlaselwa intlungu kunokuphinda ngokuphindaphindiweyo ngalo lonke usuku, ngaphandle kwendawo ecacileyo. Ngokuqhelekileyo, ukucabisa, ukuhlanza kunye nomkhuhlane kuyaqaphela. Kwiimeko ezinqabileyo, ukuphuma kwamathambo okanye emathunjini kunokwenzeka.

Ngamanye amaxesha nge-vasculitis enomzimba, inkunzi okanye ezinye izitho (imiphunga, intliziyo, neempahla zengqondo) zichaphazelekayo. Ubunzima bezilonda zinokuba zihluke kakhulu - ukusuka kwizinto ezincinci, ukuya kumodareyitha kunye neemeko ezinzima.

I-vasculitis engama-hormone kubantwana: unyango

Ubume kunye neendlela zonyango ziyahlukahluka ngokuxhomekeka kwisigaba kunye nesimo sesifo (icala lokuqala, ukuphindaphinda kwesi sifo okanye ixesha lokuxolelwa), kwimbonakalo yeklinikhi kunye nobunzima, kunye nobude kunye nesimo sekhosi yesi sifo. Kodwa kusenokwenzeka ukuba ungabhalisanga i-regimen yonyango jikelele.

Kuzo zonke iintlobo zesifo, i-antigregregants isetyenziswa. Yenza i-kurantil (persanthin, dipyridamole) amaxesha amane ngosuku ngemilinganiselo ye-5-8 mg kilogram yesisindo somzimba, i-trental (agapurine, pentoxifylline) amaxesha amathathu ngosuku ngemilinganiselo yomzimba ka-5-10 mg / kg. Kwiimeko ezinzima, zombini iindidi zamachiza zinokulawulwa ngokufanayo. Ubungakanani benkqubo yezokhuseleko lunokuhluka - ukusuka kwiinyanga ezi-2 ukuya kwezi-12, ngokuxhomekeka kubukhulu besifo. Xa ifomu engapheliyo ikhetha izifundo eziphindaphindiwe rhoqo (ngekota nganye okanye ezintandathu ezintandathu).

I-anti-coagulants isetyenziswe kwisilinganiselo ngasinye, ama-activator of fibrinolysis, i-enterosorbents, i-glucocorticosteroids, i-membrane stabilizers, i-cytostatics, i-antihistamines. Ukusetyenziswa kwonyango kunye ne-plasmapheresis nazo zisetyenziswa. Ukukhethwa kweziyobisi kunye neendlela zokonyango kufuneka zenziwe kuphela ngugqirha, ukuzonyanga okanye ukulungiswa okungagunyazisiyo kwirejimenti yonyango ngaphandle kokubonisana neengcali kunye nokulawulwa kwezonyango akuvumelekanga.

Ukuthintela i-vasculitis enegazi

Inendima ebalulekileyo ekukhuselweni kwesi sifo kukuthintelwa, ukuthintela ukunyanzeliswa kwee-foci ezithathelwanayo, ukuhlukana kweso sifo. Izigulane azenzi iisampuli nge-antigens ezinobungozi (uvavanyo lweBurne, tuberculin, njl.). Ukuthintela i-vasculitis enomdla kubantwana kubalulekile u-hypoallergenic, ukungabikho ukutya, ukutya okunesondlo kunye nendlela yokuphila enempilo.