Ngelishwa, rhoqo i-galactosemia kubantwana abasandul Nangona kunjalo, imeko yezigulane ezinezifo ezixhomekeke ekuzaleni izifo zikhula ngokukhawuleza kwiintsuku zokuqala zobomi babo. Ngosuku lwesine lwenkqubo engalawulekiyo yesifo, iintsana ezinjalo azikwazi ukusela. Ukuziphatha kwabo okungenakukhathazeka, okubonakalayo ukusuka kude, kubangelwa yimeko engaphakathi yangaphakathi - banokunyuka kwesibindi, i-jaundice ibonakala, i-fluid iqokelela kwiifom.
I-Galactosemia sisifo esibi, asikwazi ukunyangwa ngendlela yokuphathwa kwezifo zentsholongwane, kodwa kunokwenzeka ukudala umntwana onokuthi uxilongwe ngegama elifanayo kunye neontanga zakhe ezinempilo. Kule meko, uncedo oluphela lunokunikwa umntwana kukuba ufunde indlela yokulandela ukutya okhethekileyo okuyimfuneko kumntwana.
Iingxaki kunye neZigotypho zeGalactosemia
I-Galactosemia iyisifo esizalwe ngumntu (esibangelwayo) esibangelwa ngumonakalo we-metabolism kwaye ekhokelela ekuhlanganyeleni kwe-galactose emzimbeni. Ngenxa yesifo se-genetic galactosemia, ukuguquka kwe-galactose ukuya kwi-glucose ayiphumeleli.
Iintsana ezininzi ezisandul 'intsha ezine-galactosemia zinesisindo esikhulu somzimba - ngaphezulu kwama-5 kilogram. Emva kokusondla, bahlanza kakhulu, kwaye ngamanye amaxesha urhudo. Iimeko zezigulane zihlahloka ngokukhawuleza ngenxa yokunyuka kwesibindi, i-pleen, i-ascites (imeko apho umbane uqokelela kwisigxina esiswini). Kamva, iimpawu zihamba kunye ne-clouding ye-lens (okanye i-cataract). Ngaphandle kwonyango, iintsana ezisuka kwi-galactosemia zingafa ngenxa ye-bacterial sepsis, esoloko ikhula nale sifo. Nangona kunjalo, kwiimeko zanamhlanje, izigulane ezineempawu zokuqala ze-galacosemia zikuncedwa ngokukhawuleza ngabasebenzi bezonyango.
Unyango lwe-galactosemia - ukutya okunzulu
Isiseko sokonyango kwabantwana abagulayo kukutya okungekho mveliso. Hlalani nikhumbule ukuba ngelixa abantwana be-lactose abangenayo i-lactose-free-milk, i-milk-free-free products are not allowed for newborns with galactosemia. Ekudleni komntwana, kuyimfuneko ukukhusela ubuncinane obunobisi kunye neziphumo zayo, kuquka ukuxuba ubisi - abanakukwazi ukungena ngaphakathi emzimbeni womntwana. Imixube engasetyenziselwa i-galactosemia yimixube ye-soy kunye nobisi lwe-almond.
Nangona kunjalo, gcina ukhumbule ukuba ukukhishwa kweemveliso zobisi ezifana neeshizi, i-yogurt, ukhilimu, ibhotela, kunye neemveliso ezinemizila yobisi - oku akukona umlinganiselo wesikhashana. Kule mveliso, isigulane esinomdla we-galactosemia kuya kufuneka siguqule ubomi bakhe bonke, igweme ukubandakanya iimveliso ezinjengegargarine, isinkwa, i-sausages kunye nemveliso egqityiweyo, apho kubonakala khona ubisi. Musa ukudimazeka, ungasebenzisa uluhlu olubanzi kunazo zonke iimveliso: inyama, intlanzi, imifuno, iziqhamo, i-oli yemifino, amaqanda, iindidi ezahlukeneyo.