I-funicular myelosis yintlungu yesigxina esichaphazela iimbambo zayo zangaphambili. Kwiimeko ezininzi, eso sifo senziwa kunye ne-perinzic anemia. Ixesha eliqhelekileyo, ukuguqulwa okuhlangeneyo yindlela egameni lesi sifo - ifunyanwe kubantu abangaphezu kweminyaka engamashumi amane ubudala. Izigulane zezilwanyana ezincinci ziba nzima ukugula.
Iimbangela ze-funicular myelosis
Isizathu esibalulekileyo sesifo soxilongo - lenye enye igama eliqhelekileyo lesi sifo - kukunqongophala kwe-vitamin B12 kunye ne-acid ye-folic emzimbeni.
I-Cyanocobalamin iza kunye nokutya. Kuba ukuxutywa kwayo kwindlela yokuxhamla isisu kudibanisa into yangaphakathi yeNqaba. Olu hlobo lokugqibela luveliswa ngeengqungquthela ezisemkhatsini wegastric mucosa. Ngako oko, ukuba iimbonkqo ziyeka ukusebenza kakuhle, i-vitamin B12 ayinako ukuxutywa.
Ukuxhomekeka kwi-syndrome ye-funicular myelosis zizinto:
- Achilles gastritis;
- i-diphyllobothriasis;
- gastroectomy;
- isifo seliliac;
- Sesifo sikaCrohn;
- isifo sofuba;
- Pellagra;
- malabsorption syndrome;
- i-diverticulosis yamathumbu.
Ekubeni amaxesha amaninzi izigulane ezine-funicular myelosis zifunyaniswa zizifo ezizimele, kukho isizathu sokukholelwa ukuba ukungadibanisi kwisistim somzimba kungakhokelela ekulahlekeni kwe-cyanocobalamin.
Iimpawu ze-funicular myelosis
Esi sifo sinobuchule obuninzi. Phakathi kwazo:
- hypotension;
- Ukuphazamiseka emsebenzini wezitho zeplavic;
- i-flaccid paresis;
- ubuthathaka emilenzeni ;
- i-ataxia (ukulungelelanisa ukusebenzisana);
- ukugada kwamalungu;
- ukuvakalelwa kwezandla kunye neenyawo;
- ukwanda kwetekon reflex.
Ukuxilongwa kunye nokunyangwa kwe-funicular myelosis
Ukufumana ukudibanisa kokunciphisa, ingcali ayisanele ukuphulaphula izikhalazo. Diagnostics ziquka:
- uviwo lwesisu;
- ukuhlolwa kwegazi okupheleleyo (ukufumana isantya se-anemia kunye nokungabikho kwe-vitamin B12);
- ukuxilongwa ngokuhlukileyo;
- uphando lwendalo kunye nobukho bobuthathaka obufihlakeleyo.
Unyango lwe-funicular myelosis kufuneka lujoliswe ekupheliseni imbangela eyabangela ukubonakala kwayo:
- Ukubuyiselwa kwinqanaba le-cyanocobalamin lijojowe kumanani amakhulu.
- I-acid ye-folic imiselwe izigulane 5-15 mg ngosuku.
- Ngenxa yethoni ye-muscle eyongeziweyo, kucetyiswa ukuba uphuze iBlolofen, Midokalm , Seduxen.