Izifo ze-Giringsprung kubantwana

Isifo sikaHirschsprung sisifo esibizwa ngokuba ngumntu ososayensi uHarold Girpshrung, owathi waqala ukumchaza. Namhlanje, leli gama liye ligama lomntu kunye nabantu abambalwa baya kwintsikelelo yalo, ngoko ke babhala ngokukodwa kwileta encinci.

Ngelishwa, isifo sikaHirschsprung kubantwana yinkinga eqhelekileyo kakhulu ukuba iintsana kunye nezingane zasenkulanga kufuneka zijamelane nazo. Ngamanye amaxesha kufunyanwa ngabantu abadala. Ngokuqhelekileyo, isifo sikaHirschsprung kubazali abasandul 'ukuzalwa siyabhalwa ngenxa yokungondleki, esichazwa ngokuqhaqhaqhayisa, ukunyaniseka. Kwaye kuyingozi kakhulu, kuba isifo sineengxaki kunye nokufa kuhleliwe.

Esi sifo sisifo semfuyo, oko kukuthi, ilifa elivela kubazali. Kule meko, abathwali be-gene bazingakwazi ukugula. Ngokuqhelekileyo ukuxilongwa kwesifo sikaHirschsprung siphela ngokuqinisekiswa kweengcamango malunga namakhwenkwe. Bahlala begula ngokuphindaphindiweyo, baze bagule emva kokuzalwa. Ukufumanisa kwesi sifo kumantombazana kuyinto engekho.

Iimpawu ezimele zilumke

Ingundoqo yesifo sikaHirschsprung kukuba kwindawo ethile yamathumbu ayikho iziphetho zentsholongwane eziqinisekisa ukugqithiswa kwe-stool ngenxa yokuchasana okunjenge-wave. Ngenxa yesi sizathu, ukutya okugayiweyo akugciniweyo, kuqokelela emathunjini. Oku, kunjalo, yimbangela yokwelula udonga lwamathumbu. Iimpawu eziphambili zesifo seHirschsprung kubantwana ziqhenqelekanga, zihamba kunye nehudo, ukuhlambalaza, ukuhlanza kunye nentlungu. Umntwana ngokukhawuleza wenza i-frog isisu. Isibilini esivuvukalayo sibonakala ngaphandle kobunzima, kwaye xa ucinezela esiswini, ngoko i-skinblock ikwazi ukuva ukuhamba kwebilini. Ukuba kukho enye yale mpawu ifumaneka, unyango lwesifo seHirschsprung kubantwana kufuneka siqale ngokukhawuleza. Ukuba oku kungenziwa ngokukhawuleza kunokwenzeka, imeko yonke yomntwana iya kuhlahloka ngokukhawuleza. Umntwana uya kukhawuleza alahlekelwe isisindo, abe nexhala, athukuthele. Kwixesha elizayo, kunokubakho ingqondo yengqondo, ukuphuhliswa kweengxaki ezingakhange zilungiswe ngengqondo.

Izindlela kunye nokusebenza kwonyango

Ngaphambi kokuba ugqirha umisele umntwana unyango lwenkqubo, kuyadingeka ukuba uhlolisise ngokufanelekileyo isifo. Ngenxa yokuba isifo sikaHirschsprung sinesimo semvelo kwaye sizuze ilifa, ngoko njengendlela yophando lwebhubhoratri, i-histology isetyenziswe, oko kukuthi, isifundo seeseli kunye nezicubu kwiindawo ezichaphazelekayo. Abazali kufanele balungiselele umntwana ukuba abe ne-biopsy. Emathunjini, oogqirha baya kuzisa inkqubo ekhethekileyo. Inaliti ekupheleni kwayo iya kusivumela ukuba sitshintshe iqhekeza elincinci le-intestinal mucosa. Xa kwenzeka ukuba ukuxilongwa kuqinisekiswe, umntwana usalindele inkqubo eninzi kunye neyinkqubo enonyango. Unokwenza ngaphandle kwe-biopsy. Ukuqinisekisa ukucinga, i-x-ray yokuvuvukala amathumbu, eninzi kunye namathole.

Ukulungiswa kwesifo sikaHirschsprung sinokuqhutywa ngokuzimeleyo, kodwa le ndlela ayiyi kusombulula ingxaki kanye kanye. Ukuphucula imeko epheleleyo yomntwana, oogqirha bacebisa ukudibanisa unyango kunye nokusikwa, ukuguqulwa kwe-physiotherapy, ukuvuselela umonakalo we-peristalsis. Kubalulekile ukulandela ukutya okuxhasayo, okusekelwe ekusetyenzisweni kokutya kwezityalo, iimveliso zobisi ezinomuncu, inyama. Qiniseka ukugcina ukutya komntwana kwimveliso yokuvelisa igesi. Ukuba ngumntwana oncelisayo, ke yonke le mithetho kufuneka ibonwe ngumama.

Ngelishwa, kuphela ukusebenza kunye nesifo sikaHirschsprung kuya kunceda ukususa ukuxilongwa, ngexesha apho indawo echaphazelekayo iya kususwa emathunjini.