Uninzi lwezidumbu ze-systemic ziyinqabile kakhulu, kwaye abaninzi abantu abazi lutho ngabo. Enye yezi zifo ziyi-vasculitis - luhlobo luni lokugula, yintoni imiqondiso, imiphumo kunye nokunyangwa kwezigulane kwizigulane ngokuqhelekileyo ezingaziwa. Ngoko ke, phambi kokuqala kwonyango, uphando luqhuba ukubonisana ngokubanzi kunye nokuthatha inxaxheba ekufuneka kuthathe inxaxheba kwi-immunologist, kuba i-pathogenesis yenkqubo yokuzikhusela yomzimba isentliziyweni yesifo.
Yintoni le "isifo se-vasculitis", kwaye ziziphi iimpawu zayo?
Ukuchazwa kwesifo yiqela elipheleleyo lezifo ezidibanisa iindlela eziqhelekileyo zokukhubazeka - ukuvuvukala kweendonga zeetriyeri, i-capillaries, i-venules, i-arterioles kunye nemithanjeni. Enyanisweni, i-vasculitis isifo seemithwalo yegazi kunye negazi eliza kuzo kwiithambo ezinqamlekileyo kunye nezitho ezenza utshintsho olusesikweni.
Ukwahlula okulula kwesifo:
- I-vasculitis yeprayimari ukuvuvukala kwemimandla yegazi ehamba ngokuzenzekelayo ngenxa yezizathu ezingaziwa.
- Izidumbu ze-vasculitis - izifo zentsholongwane ezibonakalayo ekuphenduleni ezinye izifo.
Kwimichiza, isifo esibuzwayo sichazwa ngale ndlela:
1. I-Vasculitis yeenqanawa ezincinci:
- I-Charge-Strauss syndrome okanye i-eosinophilic granulomatosis kunye ne-polyangiitis;
- isifo se-GBM;
- vasculitis ye-cryoglobulinemic;
- Isifo sika-Wegener okanye i-granulomatosis nge-polyangiitis;
- I-Immunoglobulin-A-vasculitis okanye i-Shonlein-Genocha ebomvu;
- anti-C1q-vasculitis okanye i-hypocomplexary urticaria syndrome;
- polyangiitis microscopic.
2. I-Vasculitis yeenqanawa eziphakathi:
- i-nodular periarteritis okanye i-nodular polyarteritis;
- Isifo seKawasaki .
3. I-Vasculitis yeenqanawa ezinkulu:
- arteritis Takayasu;
- Isifo sikaHorton okanye i-cell arteritis enkulu.
4. I-Vasculitis yeenqwelo zobukhulu obuhlukeneyo:
- Isifo sikaKogan;
- Isifo seBehcet.
5. I-Vasculitis yezitho:
- arteritis;
- I-angiitis ephambili yenkqubo ye-nervous central;
- aortitis;
- nge-leucocytoclastic cutan angiitis kunye nabanye.
6. I-vasculitis yesistim:
- rhumatoid;
- lupus;
- sarcoidosis nabanye.
7. I-vasculitis yesibini:
- ezinxulumene neentsholongwane;
- i-paraneoplastic;
- ezinxulumene namayeza nabanye.
Iimpawu eziqhelekileyo zempilo:
- ubushushu obuphakamileyo;
- iphosa;
- ukukhathala;
- ukungabi nesidlo;
- ubuthathaka.
Umfanekiso othile weklinikhi wesifo se-vasculitis kuxhomekeke kwiintlobo ezahlukeneyo, izitho ezichaphazelekayo kunye neenkqubo, ubunzulu bokuvuvukala nezinye izinto. Ngoko ke, kuphela ugqirha onokwazi ukuxilonga lesi sifo ngesiseko seemvavanyo zemizimba, iimvavanyo zelabhoratri, izifundo zophando.
Yiyiphi i-vasculitis ye-allergenic?
Njengoko igama libonisa ukuba, uhlobo oluthile lwe-pathology ukuvuvuka kwemithambo yegazi malunga nemvelaphi yeempendulo. Uphawu oluphambili - ulusu lwekhumba, olunokuthi lube noluntu ohlukileyo. Ngokuhambelana nayo, i-vasculitis ye-allergen ibonwa njengesifo esahlukileyo, ihlelwa kwiindidi ezininzi:
- i-erythema nodosum - ukubonakala kwamatywina phantsi kwesikhumba shin;
- I-Arteriolitis Rutera - i-rashes ngohlobo lwamaphepha, amabala, "iinkwenkwezi", idibanisa kunye nempilo embi;
- isifo se-vasculitis - ukuba iimpawu zihambelana nesi sifo asikaziwa, ngokuqhelekileyo kufumaneka ngengozi kwi-dopplerography (kwiinqanawa zikhona i-microthrombi);
- i-hemosiderosis - ukubonakala kwe-brown-brown brownmentation kwesikhumba;
- isifo se-vasculitis - ukufa ngokukhawuleza kwezicubu emva kokuqala kwe-epidermis rash.
Iyintoni le "vasculitis ye-rhumatoid"?
Olu hlobo lweentsholongwane luhlobo oluthile lokuvuvukala kweendlela zengxande ze-vascular, ukuphuhliswa ngenxa yokuqhubela phambili kwesifo se-rheumatoid arthritis.
Kuyaziwa ukuba lolu hlobo lwe-vasculitis lujongene nezifo zemiphunga, inkqubo yeentlanzi, isikhumba kunye nomonakalo wezandla, ukuhluleka kwentliziyo (pericarditis). Nangona kunjalo, iimpawu ezicacileyo zesifo ziyabonwa zingaphantsi kwe-1% yezigulane, ngoko ke uhlobo oluchaziweyo lwenkqubo yokuvuvukala lufunyenwe kakade kwizigaba ezidlulileyo, okwenza kube nzima ukuphatha i-rheumatoid arthritis kunye ne-vasculitis.