Esi sifo sibizwa ngokuba yi-pneumonia ephazamisayo kunye nephritis, i-pulmary hemorrhage okanye idiopathic hemosiderosis. Igama langempela liyi-Wellpasture's syndrome. Esi sisifo esingavamile kakhulu esichaphazela umntu omnye kwisigidi. Kodwa ke kufuneka ukwazi malunga neempawu zalo, iimpawu kunye neendlela zokonyango.
Izizathu eziphambili kunye neempawu ze-Goodpasture Syndrome
Esi sisifo esiyinkimbinkimbi esisisigxina esichaphazelekayo kunye nezilonda zeembalo ze-basal ze-alveoli yamaphaphu. Okucacileyo ngakumbi, isifo sifana nabantu abane-immunity ekhuselekile kwaye ibonakaliswe yimpompo. I-diagnostic Wellpasture syndrome eyaqhelwaniswa kakhulu kwaye ininzi yabagulayo-abatsha abantu. Esi sifo sithanda amadoda phakathi kweminyaka eyi-18 no-35.
Umsebenzi wezenzululwazi kunye neengxelo ze-Goodpasture's syndrome sele zibhalwa ngokubanzi, kodwa akukho nzu lulwazi oye wakwazi ukusombulula isizathu sesifo. Kuyaziwa ngokuqinisekileyo ukuba i-syndrome isekelwe ekubunjweni kwamanqindi anqamlekileyo, echaphazelayo, okuchaphazela iinkqubo zeekhemikhali eziyinkimbinkimbi emzimbeni. Konke oku ngenxa yoko kubangela umonakalo kwindonga ye-vascular.
Kukho iziphakamiso zokuthi i-Wellpasture's syndrome ingabangela ukusuleleka kwintsholongwane okanye ibhaktheriya (njengokuthi, umzekelo, intsholongwane yegciwane). Ukongezelela, izinto zangaphandle nazo zingaba nefuthe elibi kumasosha omzimba. Njengoko uqeqesho luye lwabonisa, ababhemayo kwi-hemorrhage ye-intrapulmonary babandezeleka rhoqo. Ingozi kunye nabantu abasebenza kwindawo kunye neendawo ezinobungozi bemichiza, kunye nalabo abathabatha imithi ethile, bavezwa.
Ukuphikisana malunga nezizathu zesifo, asimele sikhohlwe malunga nokusetyenziswa kwemfuyo, nangona kwimeko yesifo se-Goodpasture le nguqulo inokuba yiphutha. Kwaye ezinye iingcali zikholelwa ukuba esi sifo sibheka kwimvelaphi ye-hypothermia rhoqo.
Iimpawu zokuqala zesifo se-Goodpasture zifana kakhulu nokubonakaliswa kwezilwanyana zamathambo zendalo. Isici esibalulekileyo sophuhliso luphuhliso olukhawulezayo. Ngokungafani nesimo esiqhoqhoqhobisayo, isifo se-Wellpasture syndrome ukusuka ekuqaleni ukuya kwisigaba esinqatshelwe kakhulu sinokuqhubeka kwimiba yeentsuku.
Imbonakalo ebalulekileyo yesi sifo iquka:
- i-hemoptysis (ngamanye amaxesha igazi le-veins libonakala kwi-sputum, ngamanye amaxesha amancinci egazi amancinci afunwa);
- buthathaka;
- ukulahlekelwa ngumthetho;
- ukuphefumula okufutshane ;
- ukuvakalelwa okungathandekiyo esifubeni;
- ukuhla okubukhali ekuziphatheni komzimba;
- ukwanda kweqondo lokushisa;
- ukuphuhliswa kwengqondo;
- ukuhla kwe-hemoglobin.
Ukuxilongwa kunye nokunyangwa kwe-Wellpasture's syndrome
Ukuba awuyikuphulaphula isifo se-Goodpasture, ngoko isifo singakhokelela ekufeni. Ukuze ugweme unyango olude kwaye lunzima kakhulu, kunye nokusola ukuqala kukufuna ukunxibelelana nengcali. Ukujonga
Kwigazi legulane, isifundo siya kuba nako ukucacisa ubukho bezilwanyana ezithile. Ukongezelela, ukukrokra kungabangela ukunciphisa i-hemoglobin kunye namanqanaba aphakamileyo egazi elibomvu. Kuvavanyo jikelele lwegazi lwe- Goodpasture's syndrome kubonisa inani elikhulu leprotheni. Kwi-roentgenogram iindawo zokuvuvuka zibonakala ngokucacileyo.
Unyango lwe-Wellpasture's syndrome nakwiiyure zokuqala mazibe nzima. Ngokuqhelekileyo inkqubo yokonyango ibandakanya iziyobisi ze-hormonal kunye ne-istiostatics. Ezinye izigulane kufuneka zibonise i-substitution-thérase-transfusion ye-plasma kunye nobunzima be-erythrocyte. Ukuba i-syndrome ivuselela umsebenzi wezintso ezincitshisiweyo, i-dialysis, ngamanye amaxesha nokutshintshwa, kunokufuneka.