Esi sifo esingaqhelekanga. Isifo se-Badda-Chiari sifumaneka kumntu omnye kwiwaka eziliwaka. Esi sifo sidibene nokungahambi kakuhle kwesibindi. Ininzi kaninzi itholakala kwindoda ephakathi kwamabhinqa. Kodwa ngezikhathi ngezifo, izigulane ezincinci nazo ziyafikelela.
Iingxaki zeBadda-Chiari Izifo
I-Badda-Chiari syndrome - ukuphazamiseka kwemifuno ye-hepatic. Ngesi sifo, iimvumba zincinci, ngenxa yokuba igazi eliqhelekileyo kwisibindi liphazamiseka. Ngelo xesha, umzimba awukwazi ukusebenza ngokufanelekileyo.
Isizathu sesi sifo sinokungabikho kwamalungu omzimba we-hepatic veins. Ezi zinto zilandelayo zifaka isandla ekuphuhliseni i-syndrome:
- nzakala;
- iimvumba;
- i-cirrhosis;
- i hepatitis;
- i-hepatocellular carcinoma;
- peritonitis;
- i-vasculitis;
- khulelwa;
- kubeleka;
- pericarditis;
- thrombosis;
- izifo ezithile;
- polycythemia .
I-Budda-Chiari syndrome inokuphuhlisa kwimvelaphi yokusetyenziswa kwexesha elide okanye emva kokungenelela kokuphaphazelekayo. Ngamanye amaxesha isifo sibonakala emva kokukhulelwa nokubeletha.
Iimpawu zeBadd-Chiari Syndrome
Ukwahlula phakathi kweendlela eziluhlaza kunye nezifo ezingapheliyo zesifo. Oku kuvela kwiimeko ezininzi. Ukubonakaliswa kwesi sifo kuyahluka ngokuxhomekeka kwimoko yayo. Ngoko, umzekelo, ukugula okungapheliyo kweBudda-Chiari kunokuhlala kungabonwa. Kwaye kwinqanaba elisemva kukho iziganeko ezifana neentlanzi, ukuhlanza, ukuvakalelwa kwintlungu kwi-hypochondrium efanelekileyo. Isibindi
Ifomu elimangalisayo likaBudd Chiari libonakaliswa yimpawu ezifana nobuhlungu obukhulu kunye nokuhlanza. Xa isifo sisasazeka emithanjeni engezantsi, isigulane sinokuba yimilenze yokuvuvukala, i-reticulum ye-vascular ibonakala eludongeni lwangaphakathi lomzimba. Esi sifo sikhula ngokukhawuleza, kwaye kwiintsuku ezimbalwa isigulane sinokuthi sifumaneke nge-ascites.
Impawu yezifo ezininzi zesibindi, isibonakaliso - i-jaundice - ayinqabile kwisifo seBuddha-Chiari.
Unyango lwe-Badda-Chiari syndrome
Kwimigangatho yokuqala, unyango lwezokwelapha lucacisiwe, olubandakanya ukusetyenziswa kwezidumbu ze- diuretics kunye nama-coagulants, kodwa akusoloko inika iziphumo ezilungileyo.
Ngokuqhelekileyo, isifo se-Badda-Chiari siphathwa ngokugqithisileyo kwisibhedlele. Eyona ndlela ikhethekileyo kukusetyenziswa kwe-anastomosis. Kwiimeko ezithile ezinzima, ukufakelwa kwesibindi kunokufuneka.